Pulmonary Alveolar Proteinosis A Rare Disease
Pulmonary Alveolar Proteinosis A Rare Disease
Keywords:
Alveolar Proteniosis, PulmonaryAbstract
Pulmonary alveolar proteinosis is a rare lung disease in which abnormal accumulation of surfactant occurs with in the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy , pulmonary infection, or environmental exposure to dusts or chemicals. Rare familial forms have also been recognized suggesting a genetic component . we are going to present a rare case of pulmonary alveolar proteinosis.
References
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3. Stanley E, Lieschke GJ, Grail D, et al. (June 1994). "Granulocyte/macrophage colony-stimulating factor-deficient mice show no major perturbation of hematopoiesis but develop a characteristic pulmonary pathology". Proc. Natl. Acad. Sci. U.S.A. 91 (12): 5592–6. doi:10.1073/pnas.91.12.5592.
4. Uchida K, Beck D, Yamamoto T, Berclaz P, Abe S, Staudt M, Carey B et al. (2007). "GM-CSF autoantibodies and neutrophil dysfunction in pulmonary alveolar proteinosis". N Engl J Med 356 (6): 567–79. doi:10.1056/NEJMoa062505. PMID 17287477.
5. Monisha Das, MD And Gary A. Salzman, MD (February 2010). "Pulmonary Alveolar Proteinosis: An Overview for Internists and Hospital Physicians". Hospital Practice. 38 (1): 43–49. doi:10.3810/hp.2010.02.277. PMID 20469623.
6. Ramirez-Rivera J, Nyka W, McLaughlin J (1963). "Pulmonary Alveolar Proteinosis: Diagnostic
Technics and Observations". New England Journal of Medicine 268 (4): 165–71. doi:10.1056/NEJM196301242680401. PMID 13990655.
7. Ramirez-Rivera J, Schultz RB, Dutton RE (1963). "Pulmonary Alveolar Proteinosis: A New Technique and Rational for Treatment". Archives of Internal Medicine 112: 173–185.
8. Ceruti M, Rodi G, Stella GM, et al. (2007). "Successful whole lung lavage in pulmonary alveolar proteinosis secondary to lysinuric protein intolerance: a case report". Orphanet J Rare Dis 2: 14. doi:10.1186/1750-1172-2-14 PMC 1845139 PMID 17386098.
9. Menard KJ (April 2005). "Whole lung lavage in the treatment of pulmonary alveolar proteinosis" J. Perianesth. Nurs. 20 (2): 114–26. Doi 10.1016/j.jopan.2005.01.005 PMID 15806528.
10. Inoue Y, Trapnell BC, Tazawa R,et (April 2008). "Characteristics of a Large Cohort of Patients with Autoimmune Pulmonary Alveolar Proteinosis in Japan". Am. J. Respir. Crit. Care Med. 177 (7): 752–62. doi:10.1164/rccm.200708-1271OC. PMC 2720118. PMID 18202348.
2. Griese M, Brasch F, Aldana VR, Cabrera MM, Goelnitz U, Ikonen E, et al. Respiratory disease in Niemann-Pick type C2 is caused by pulmonary alveolar proteinosis. Clin Genet. Feb 2010;77(2):119-30.
3. Stanley E, Lieschke GJ, Grail D, et al. (June 1994). "Granulocyte/macrophage colony-stimulating factor-deficient mice show no major perturbation of hematopoiesis but develop a characteristic pulmonary pathology". Proc. Natl. Acad. Sci. U.S.A. 91 (12): 5592–6. doi:10.1073/pnas.91.12.5592.
4. Uchida K, Beck D, Yamamoto T, Berclaz P, Abe S, Staudt M, Carey B et al. (2007). "GM-CSF autoantibodies and neutrophil dysfunction in pulmonary alveolar proteinosis". N Engl J Med 356 (6): 567–79. doi:10.1056/NEJMoa062505. PMID 17287477.
5. Monisha Das, MD And Gary A. Salzman, MD (February 2010). "Pulmonary Alveolar Proteinosis: An Overview for Internists and Hospital Physicians". Hospital Practice. 38 (1): 43–49. doi:10.3810/hp.2010.02.277. PMID 20469623.
6. Ramirez-Rivera J, Nyka W, McLaughlin J (1963). "Pulmonary Alveolar Proteinosis: Diagnostic
Technics and Observations". New England Journal of Medicine 268 (4): 165–71. doi:10.1056/NEJM196301242680401. PMID 13990655.
7. Ramirez-Rivera J, Schultz RB, Dutton RE (1963). "Pulmonary Alveolar Proteinosis: A New Technique and Rational for Treatment". Archives of Internal Medicine 112: 173–185.
8. Ceruti M, Rodi G, Stella GM, et al. (2007). "Successful whole lung lavage in pulmonary alveolar proteinosis secondary to lysinuric protein intolerance: a case report". Orphanet J Rare Dis 2: 14. doi:10.1186/1750-1172-2-14 PMC 1845139 PMID 17386098.
9. Menard KJ (April 2005). "Whole lung lavage in the treatment of pulmonary alveolar proteinosis" J. Perianesth. Nurs. 20 (2): 114–26. Doi 10.1016/j.jopan.2005.01.005 PMID 15806528.
10. Inoue Y, Trapnell BC, Tazawa R,et (April 2008). "Characteristics of a Large Cohort of Patients with Autoimmune Pulmonary Alveolar Proteinosis in Japan". Am. J. Respir. Crit. Care Med. 177 (7): 752–62. doi:10.1164/rccm.200708-1271OC. PMC 2720118. PMID 18202348.
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Published
2013-10-31
How to Cite
Kumar, N., K, J., Ranjan, S., Varshney, A. N., & Anand, A. (2013). Pulmonary Alveolar Proteinosis A Rare Disease: Pulmonary Alveolar Proteinosis A Rare Disease. National Journal of Integrated Research in Medicine, 4(5), 102–104. Retrieved from http://nicpd.ac.in/ojs-/index.php/njirm/article/view/604
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Case Report
