An Extremely Rare Presentation Of Central Arterial Stiffness With Kartagener Syndrome In A Young Female: An Unseen Comorbidity
Presentation Of Central Arterial Stiffness With Kartagener Syndrome In A Young Female
Primary Ciliary Dyskinesia (PCD) is an autosomal recessive hereditary disorder having wide range of genetical and phenotypical expression. The triad of situs inversus, chronic sinusitis and bronchiectasis is known as Kartagener syndrome (KS). We report the case of 22 year old unmarried female presented with the typical triad diagnosed as Kartagener syndrome with positive saccharine test associated with extremely rare presentation of moderate to high central arterial stiffness, recognised as previously unreported fatal co morbidity in a young age. Treatment of bronchiectasis, sinusitis as well as hypo- Vitaminosis D has been commenced with promising response in follow up. [Rana R Natl J Integr Res Med, 2019; 10(6):85-88]
This work is licensed under a Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International License.