Primary Intramedullary Primitive Neuroectodermal Tumor Of Spine– A Rare Clinical Presentation

Abstract

Primitive neuroectodermal tumors (PNETs) are a group of malignant neoplasms which were initially defined by Hart and Earle in 1973. PNETs most commonly occur in the cerebellum but can arise in the pineal gland, cerebrum, spinal cord brain stem, and peripheral nerves. Intraspinal PNET is extremely rare and histologically indistinguishable from other neural axis PNETs. A a multitude of therapeutic strategies have been employed with varying success. We report a case of Primary intraspinal PNET which was rare location in the intramedullary region with review of literature.