Anaesthetic Management of Hunter Syndrome with AmbuLMA

Abstract

Patients with Hunter Syndrome have multisystem involvement and difficult airway due to infiltration of tissues with mucopolysaccharides. A eight year old, male child with Hunter Syndrome weighing 20 kg was admitted for repair of umbilical hernia and right inguinal hernia. Anaesthetic management was planned with IV induction and a 2.5 size Ambu Laryngeal Mask Airway (LMA). Post-operatively child was observed for 24 hrs and LMA was removed when the child was fully awake. Children with mucopolysaccharidosis are prone to atlantoaxial subluxation. Airway management with AmbuLMA in this case demonstrated safe alternative to endotracheal intubation.