A Rare Case of adult Alveolar Rhabdomyosarcoma of the Lacrimal Sac

Case Report A Rare Case of adult Alveolar Rhabdomyosarcoma of the Lacrimal Sac- Case report

Abstract

Rhabdomyosarcoma is a common malignancy in children but rare in adults. The most common sites of involvement in adults are the extremities, genitourinary system and head and neck region. Rhabdomyosarcoma of the lacrimal sac is exceedingly rare, with only three cases ever reported in literature. A 23-year-old man presented with complaints of a painless swelling in the medial canthus of the right eye and epiphora. He was initially treated at a local hospital for acute dacrocystitis. There was no response and swelling persisted. Further evaluation including a CT scan showed a mass arising from the lacrimal sac with extension to the orbit. A core biopsy of the mass lesion revealed a lacrimal sac tumour. Histopathology and immunohistochemistry was suggestive of an alveolar rhabdomyosarcoma. He was started on chemotherapy with the IRS-4 protocol. This case report highlights the need to keep the possibility of malignancy in a case of a medial canthus mass, which responds poorly to antibiotics