Persistent Mullerian Duct Syndrome
Persistent Mullerian Duct Syndrome
DOI:
https://doi.org/10.70284/njirm.v3i1.255Keywords:
Persistent mullerian duct syndrome, male pseudohermaphroditism, maleAbstract
Persistent mullerian duct syndrome is a rare form of internal male pseudohermaphroditism in which mullerian duct derivatives are present in a genotypic (46XY) and phenotypic male. We report a rare case of persistent mullerian duct syndrome in an adult fertile male in whom mullerian duct derivatives (uterus and fallopian tubes) were found in the right hernia sac at herniotomy.
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