An Unusual Presentation of Desquamation at Birth

Abstract

Background : Incontinentia Pigmenti is a rare, X-linked dominant genodermatosis with dermal, ocular,
neurological and dental anomalies. Case Characteristics : A female newborn presented at birth with excessive
desquamation turned out to have Incontinentia Pigmenti. Message : Desquamation at birth is an unusual
presentation of IP.