Heryln - Werner - Wunderlich Syndrome associated with Rectovesical fistula and Neural tube defect: A Rare Presentation

Heryln - Werner - Wunderlich Syndrome

Abstract

Herlyn – Werner – Wunderlich syndrome (HWWS) is an uncommon combined Mullerian and Mesonephric duct anomaly, and its presentation in neonatal period is even rarer. Symptoms generally occur after menarche about 12 to 13 years old and it is usually diagnosed by pelvic magnetic resonance imaging. Our case is 1 day old asymptomatic newborn with all the features of this syndrome that came to our attention during diagnostic workup of rectovesical fistula and meningomyelocele. The aim of this article is to share our experience of coincidental association of this syndrome along with other malformations and focus the attention on the importance of high level of suspicion of HWWS in neonatal period which leads to early diagnosis and treatment.